This comprehensive text focuses on the nature of malnutrition in Cystic Fibrosis (CF), its manage-ment and prevention, and on the interrelated topic of gastroin-testinal manifestations of CF, many of which have only recently been characterized and defined. This valuable book serves as a basis for subsequent research and the institution of programs to reverse or prevent nutritional and gastrointestinal manifesta-tion. It is a welcome new text for direct-care givers of CF pa-tients, particularly physicians, gastroenterologists, and nutri-tionists as well as researchers.
"…all dietitians new to clinical practice in pediatrics or gastroenterology should gain access to this particular publication of CRC Press."
-Journal of the American Dietetic Association
PART I - PERSPECTIVES in CYSTIC FIBROSIS. Cystic Fibro-sis: "The Most Common Lethal Ge-netic Disease." Diagnosis, Clini-cal Aspects and Outcome of Cystic Fibrosis. PART II - MALNUTRITION in CYSTIC FIBROSIS. Prevalence, Importance, Clinical Features, and Relationships to Lung Dis-ease. Etiology and Pathogenesis of Malnutrition in Cystic Fibro-sis. The Nutrient Deficits and Their Consequences. Nutritional Management. PART III - GASTROIN-TESTINAL MANIFESTATIONS of CYSTIC FIBROSIS. Overview of Pathogene-sis, Pathology, and Pathophysiol-ogy. The Pancreas: Clinical As-pects and Investigation of Pan-creatic Function. Replacement Therapy for Pancreatic Insuffi-ciency. Gastrointestinal Manifes-tations. Hepatobiliary Manifes-tations of Cystic Fibrosis. Ap-pendix. In-dex.