Cystic Fibrosis: 1st Edition (Paperback) book cover

Cystic Fibrosis

1st Edition

Edited by Julian L. Allen, Howard B. Panitch, Ronald C. Rubenstein

CRC Press

44 pages | 100 B/W Illus.

Purchasing Options:$ = USD
Paperback: 9781138112612
pub: 2017-05-31
SAVE ~$16.59
Hardback: 9781439801819
pub: 2010-03-25
SAVE ~$46.00
eBook (VitalSource) : 9780429069987
pub: 2016-04-19
from $41.48

FREE Standard Shipping!


The median age of survival for those with cystic fibrosis has risen considerably in recent years. This text thoroughly examines the developments and breakthroughs which have led to this improvement in life expectancy. With a focus on the latest discoveries in the diagnosis and treatment of the disease, this book provides a comprehensive overview of the past, current and forthcoming advancements in cystic fibrosis research and clinical care.

Table of Contents




The Genetics of Cystic Fibrosis Laurence Suaud and Ronald C. Rubenstein

Ion Transport James L. Kreindler and J. Kevin Foskett

Mucus Abnormalities and Ciliary Dysfunction A. Whitney Brown and Scott H. Donaldson

Microbiology in Cystic Fibrosis Paul J. Planet and Lisa Saiman

Inflammation in the Cystic Fibrosis Lung James F. Chmiel and Michael W. Konstan

Modifier Genes of Cystic Fibrosis Mitchell Drumm


Cystic Fibrosis: Diagnosis, Sweat Testing, and Newborn Screening Brian P. O’Sullivan

Diagnostic Approach to Diseases Associated with Cystic Fibrosis Transmembrane Conductance Regulator Gene Mutations Chee Y. Ooi (Keith), Elizabeth Tullis, and Peter R. Durie

Lung Function Testing in Infants Jessica E. Pittman and Stephanie D. Davis

Assessment of Lung Function in Young Children with Cystic Fibrosis Fariba Rezaee and Clement L. Ren

Lung Function Testing in School-Age Children with Cystic Fibrosis Oscar H. Mayer and Julian L. Allen

Thoracic Imaging in Cystic Fibrosis Pulmonary Disease Molly Raske and Alan S. Brody

Clinical Manifestations and Treatment

Pulmonary Manifestations Andrew Bush

Treatment Strategies for Maintaining Pulmonary Health in Cystic Fibrosis Susanna A. McColley

Mucolytic Therapy and Airway Clearance Techniques Felix Ratjen and Craig Lapin

Pulmonary Exacerbations Don B. Sanders and Margaret Rosenfeld

Gastrointestinal Complications of Cystic Fibrosis Maria Mascarenhas and Asim Maqbool

Liver Disease Meghana N. Sathe and Andrew P. Feranchak

Nutrition Asim Maqbool, Kelly Dougherty, Alisha J. Rovner, Suzanne H. Michel, and Virginia A. Stallings

Bone Health and Treatment Nadine G. Haddad and Linda A. DiMeglio

Cystic Fibrosis–Related Diabetes and Management Andrea Kelly and Andrew C. Calabria

Other Extrapulmonary Complications and Treatment Joshua P. Needleman and Suzanne E. Beck

Chronic Respiratory Failure and the Roles of Noninvasive Ventilation and Lung

Transplantation Samuel Goldfarb and Howard B. Panitch

Gene Repair: Past, Present, and Future Christian Mueller and Terence R. Flotte

Restoration of CFTR Function with Small-Molecule Modulators Wynton Hoover and John P. Clancy

Psychosocial Considerations and Care Systems

Quality Improvement in Cystic Fibrosis Care Michael S. Schechter

Cystic Fibrosis and Infection Control Susan Rettig and Susan Coffin

Transition to Adult Care Sherstin G. Truitt and James R. Yankaskas

Reproduction, Sexuality, and Fertility Lisa K. Tuchman and Ioanna K. Gisone

A Biopsychosocial Model of Cystic Fibrosis: Social and Emotional Functioning, Adherence, and Quality of Life David Barker and Alexandra L. Quittner

Palliative and End-of-Life Care in Cystic Fibrosis Walter M. Robinson and Jeffrey C. Klick


About the Series

Lung Biology in Health and Disease

Learn more…

Subject Categories

BISAC Subject Codes/Headings:
MEDICAL / General
MEDICAL / Pulmonary & Thoracic Medicine