1st Edition

Rare Lung Diseases A Comprehensive Clinical Guide to Diagnosis and Management

Edited By Sujith V. Cherian, Anupam Kumar Copyright 2023
    238 Pages 86 Color & 64 B/W Illustrations
    by CRC Press

    238 Pages 86 Color & 64 B/W Illustrations
    by CRC Press

    238 Pages 86 Color & 64 B/W Illustrations
    by CRC Press

    This book aims to be a complete guide to diagnose, manage, and treat rare lung diseases encountered by practicing pulmonologists and trainees. It extensively covers the "more common" of the rare lung diseases, categorizing them based on developmental lung anomalies in adults, airway disorders, diffuse parenchymal lung diseases, neoplasms, rare vascular disorders, and other miscellaneous conditions. This comprehensive review facilitates the study and understanding of this complex and diverse set of disorders, focusing on differential diagnosis, evidence-based discussions of management algorithms, and thoughtful analysis of treatment options.

    Key Features

    * Reviews multiple rare lung diseases, including ones acquired congenitally to be expressed in old age

    * Enriched with case studies and illustrations to guide respiratory physicians and trainees to devise an effective treatment plan

    *Focuses on concerned investigations, with a section on the role of new procedures in management

    Chapter 1: Introduction
    Sujith V Cherian and Anupam Kumar

    Chapter 2: Developmental lung anomalies in adults
    Oriana Salamo, Logan Hostetter, Alberto A. Goizueta, Daniel Ocazionez-Trujillo, Sujith V Cherian

    Rare genetic lung diseases

    Chapter 3: Genetic infiltrative lung diseases
    Isabel Mira Avendano

    Chapter 4: Alpha-1- antitrypsin deficiency
    Vickram Tejwani, James K. Stoller

    Rare airway disorders

    Chapter 5: Benign central airway disorders
    Prince Ntiamoah, Laura Frye

    Chapter 6: Bronchiolitis
    Bilal F. Samhouri, Jay H.Ryu

    Chapter 7: Allergic Bronchopulmonary Aspergillosis (ABPA)
    Sunjay R. Devarajan, Nicola A. Hanania

    Rare pulmonary vascular diseases

    Chapter 8: Pulmonary Arteriovenous Malformations (PAVMs) and Hereditary hemorrhagic telangiectasia (HHT)
    Daniil Gekhman, Carlos Rojas, Mingkyung Kwon, Augustine Lee

    Chapter 9: Diffuse Alveolar Hemorrhage  (DAH) syndromes
    Gaurav Manek, Rendell W. Ashton

    Chapter 10: Pulmonary Veno-occlusive Disease and Pulmonary Capillary Hemangiomatosis
    Dana Gross, Akhilesh Padhye, Roberto Barrios, Sandeep Sahay


    Rare diffuse parenchymal lung diseases

    Chapter 11: Pleuroparenchymal fibroelastosis (PPFE)
    Bhavna Seth, Sonye Danoff

    Chapter 12: Immunoglobulin G4-related lung disease
    Lauren Abplanalp, Hira Iftikhar, Girish B Nair

    Chapter 13: Eosinophilic lung diseases
    Nauman A Khan, Sujith V. Cherian

    Chapter 14: Hard Metal Lung Disease and Other Rare Occupational Lung Diseases
    Mathew Zheng, Robert Marron, Sameep Sehgal

    Chapter 15: Adult Pulmonary Alveolar Proteinosis
    Katherine Richards, Anupam Kumar, Tisha Wang

    Rare diffuse cystic lung diseases

    Chapter 16: Lymphangioleiomyomatosis
     Rosa M Estrada –Y-Martin

    Chapter 17: Lymphocytic Interstitial Pneumonia and associated Cystic Lung Diseases
    Evelyn Lynn, Liam Jeremiah Chawke, Aurelie Fabre, David J. Murphy, Cormac McCarthy

    Chapter 18: Birt Hogg Dube Syndrome
    Stephan A Reyes, Rosa M Estrada Y Martin

    Chapter 19: Pulmonary Langerhans Cell Histiocytosis and other histiocytic lung diseases
    Maryam Kaous, Bihong Zhao, Isabel Mira Avendano

    Rare pulmonary neoplasms

    Chapter 20: Primary pulmonary lymphoproliferative disorders
    Bibi Aneesah Jaumally, Khalid Mohamed Ahmed, Saadia A. Faiz

    Chapter 21: Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
    Amita Avasarala, Sameer K Avasarala, Sanjay Mukhopadhyay, Subha Ghosh, Atul C Mehta

    Chapter 22: Pulmonary Amyloidosis
    Said A. Chaaban, Parijat Sen

    Chapter 23: Primary tracheal tumors
    Moiz Salahuddin, Carlos A Jimenez

    Rare pleural disorders

    Chapter 24: Unusual causes of pleural effusions
    Niranjan Setty, Nai-Chien Huan, Rajesh Thomas

    Chapter 25: Thoracic endometriosis
    Ravi Kanth Velagapudi, John Egan

    Chapter 26:  Tumours of the Pleura
    Nai-Chien Huan, Rajesh Thomas


    Dr. Sujith V. Cherian is Associate Professor of Internal Medicine, in the Division of Critical Care, Pulmonary and Sleep Medicine at the University of Texas Health-McGovern Medical School, Houston.

    Dr. Anupam Kumar is an Assistant Professor of Medicine at the Division of Pulmonary & Critical Care Medicine at Baylor College of Medicine, Houston, Texas. He is also the Director of the Interstitial Lung Diseases (ILD) Clinic at Baylor College of Medicine.